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KMID : 0860920040060010058
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Journal of the Korean Association EMG-Electrodiagnostic Medicine
2004 Volume.6 No. 1 p.58 ~ p.61
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Two Cases of Juvenile Amyotrophic Lateral Sclerosis
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Shin Hae-Won
Yang Jae-Hoon
Jung Yeon-Kyung
Kim Seung-Min
Sunwoo Il-Nam
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Abstract
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Juvenile amyotrophic lateral sclerosis (ALS) is a rarely occurring chronic motor neuron disease, characterized by combined upper and lower motor neuron symptoms /signs with the onset before 25 years old. It is known that the inheritance is either autosomal dominant, autosomal recessive or sporadic. We report 2 cases of juvenile ALS without family history who showed severe weakness in distal limbs with definite upper motor neuron signs.
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KEYWORD
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Juvenile ALS, chronic motor neuron disease
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